1. Wenxin Ou#, Yunze Zhao#, Ang Wei, Honghao Ma, Liping Zhang, Hongyun Lian, Qing Zhang, Sitong Chen, Dong Wang, Zhigang Li*, Tianyou Wang*,Rui Zhang*.Chronic Active Epstein-Barr Virus Infection With Central Nervous System Involvement in Children.The Pediatric Infectious Disease .2023.42(1).20-26.SCI |
2. Wenqian Wang, Lejian He,Runhui Wu,Jiafeng Yao,Honghao Ma,Xiaoling Cheng,Ang Wei,Hongyun Lian,Dong Wang,, Zhigang Li,Tianyou Wang,Rui Zhang.Anaplastic lymphoma kinase positive histiocytosis presenting as hemocytopenia in an infant.pediatric blood cancer..2023.70(3).e30010.SCI |
3. 程芬芬,马宏浩,焦莹,魏昂,廉红云,王冬,杨颖,赵晓曦,李志刚,王天有,张蕊.北京儿童医院改良噬血细胞性淋巴组织细胞增生症04方案疗效及安全性评价.中华儿科杂志.2022.60(8).804-809. |
4. Qing Zhang#, Yun-Ze Zhao#, Hong-Hao Ma, Dong Wang, Lei Cui, Wei-Jing Li, Ang Wei, Chan-Juan Wang, Tian-You Wang*, Zhi-Gang Li*, Rui Zhang*.A study of ruxolitinib response-based stratified treatment for pediatric hemophagocytic lymphohistiocytosis.BLOOD.2022.139(24).3493-3504.SCI |
5. Bi X#, Zhang Q#, Chen L#, Liu D, Li Y, Zhao X, Zhang Y, Zhang L, Liu J, Wu C, Li Z, Zhao Y, Ma H, Huang G, Liu X*, Wang QF*, Zhang R*.NBAS, a gene involved in cytotoxic degranulation, is recurrently mutated in pediatric hemophagocytic lymphohistiocytosis.J Hematol Oncol.2022.15(1).101.SCI |
6. Xia Lu#, Ang Wei#, Xu Yang, Jun Liu, Siqi Li, Ying Kan, Wei Wang, Tianyou Wang, Rui Zhang*, Jigang Yang*.The Role of Pre-therapeutic 18F-FDG PET-CT in Pediatric Hemophagocytic Lymphohistiocytosis with Epstein-Barr Virus Infection.Frontiers in Medicine .2022.8.1-11.SCI |
7. Ang Wei#, Xi+B2nghao Ma, Hongyun Lian, Xu Yang, Liping Zhang, Dong Wang, Sitong Chen, Qing Zhang, Zhigang Li, Rui Zhang*, Jigang Yang*, Tianyou Wang*.18F-FDG PET/CT for identifying the potential primary diseases and predicting prognosis of secondary hemophagocytic lymphohistiocytosis in children.Contrast Media & Molecular Imaging.2022. .4849081.SCI |
8. Dong Wang, Xi-Hua Chen, Ang Wei, Chun-Ju Zhou, Xue Zhang, Hong-Hao Ma, Hong-Yun Lian, Li Zhang, Qing Zhang, Xiao-Tong Huang, Chan-Juan Wang, Ying Yang, Wei Liu, Tian-You Wang*, Zhi-Gang Li*, Lei Cui*, Rui Zhang*.Clinical features and treatment outcomes of pediatric Langerhans cell histiocytosis with macrophage activation syndrome-hemophagocytic lymphohistiocytosis.Orphanet J Rare Dis .2022.17(1).151.SCI |
9. Ja-Feng Yao, Dong Wang, Hong-Hao Ma, Hong-Yun Lian, Li Zhang, Tian-You Wang, Zhi-Gang Li, Jin Jiang, Lei Cui*, Rui Zhang*.Characteristics and Treatment Outcomes of Pediatric Langerhans Cell Histiocytosis with Thymic Involvement.J Pediatr .2022.244:194.202.e5.SCI |
10. Ying Yang#, Chanjuan Wang#, Dong Wang#, Lei Cui, Na Li, Hongyun Lian, Honghao Ma, Yunze Zhao, Liping Zhang, Wei Liu, Yizhuo Wang, Wanshui Wu, Rui Zhang*, Zhigang Li*, Tianyou Wang*.Clinical study of MAP2K1-mutated Langerhans cell histiocytosis in children.Journal of Cancer Research and Clinical Oncology.2022.148(9).2517–2527.SCI |
11. Xiao-Xi Zhao, Hong-Yun Lian, Li Zhang, Hong-Hao Ma, Dong Wang, Yun-Ze Zhao, Wei Liu, Xi-Hua Chen, Tian-You Wang, Zhi-Gang Li*, Rui Zhang*.Significance of serum Th1/Th2 cytokine levels in underlying disease classification of childhood HLH .Cytokine.2022.149.155729.SCI |
12. Wenxin Ou, Ang Wei, Honghao Ma, Zhigang Li, Yunze Zhao, Liping Zhang, Tianyou Wang*, Rui Zhang*.Familial hemophagocytic lymphohistiocytosis onset as central diabetes insipidus in a child.Pediatr Blood Cancer.2022.69(10).e29684.SCI |
13. Qing Zhang#, Yun-Ze Zhao#, Hong-Hao Ma, Dong Wang, Lei Cu., Wei-Jing Li., Ang Wei., Chan-Juan Wang, Tian-You Wang*, Zhi-Gang Li*, Rui Zhang*. . A study of Ruxolitinib-response-based stratified treatment for pediatric hemophagocytic lymphohistiocytosis. .Blood.2022.epub.epub.SCI |
14. Wenxin Ou#, Honghao Ma#, Ang Wei, Yunze Zhao, Liping Zhang, Hongyun Lian, Qing Zhang, Sitong Chen, Dong Wang, Zhigang Li*, Rui Zhang*, Tianyou Wang*.Clinical significance of cerebrospinal fluid soluble CD25 in pediatric hemophagocytic lymphohistiocytosis with central nervous system involvement.Pediatr Blood Cance.2022.69(8).e29712.SCI |
15. Dong Wang, Xi-Hua Chen, Ang Wei, Chun-Ju Zhou, Xue Zhang, Hong-Hao Ma, Hong-Yun Lian, Li Zhang, Qing Zhang, Xiao-Tong Huang, Chan-Juan Wang, Ying Yang, Wei Liu, Tian-You Wang*, Zhi-Gang Li*, Lei Cui*, Rui Zhang*. Clinical features and treatment outcomes of pediatric Langerhans cell histiocytosis with macrophage activation syndrome-hemophagocytic lymphohistiocytosis. .Orphanet journal of rare diseases. .2022.17 (1).151.SCI |
16. 魏昂、张蕊.儿童继发性噬血细胞性淋巴组织细胞增生症5例临床分析.中华实用儿科临床杂志.2022.37(1).45-50. |
17. Hongyun Lian, Lei Cui, Ying Yang, Ang Wei, Hua Cheng, Na Li, Li Zhang, Honghao Ma, Xiaoxi Zhao, Tianyou Wang, Zhigang Li*, Rui Zhang*. Second-line regimen for CNS-involved pediatric Langerhans cell histiocytosis..Pituitary..2022.25(1).108-115.SCI |
18. 魏昂、马宏浩、张利平、廉红云、杜俊烨、王冬、崔蕾、欧雯欣、赵云泽、赵晓曦、张莉、李志刚、王天有、张蕊.芦可替尼联合脂质体阿霉素、依托泊苷、甲泼尼龙和/或培门冬酶治疗儿童复发/难治性噬血细胞综合征的疗效分析.中华医学杂志.2022.102(28). 2167-2172. |
19. Hui Shi#, Han He#, Lei Cui#, Egle Kvedaraite, Zhilei Bian, Tao Huang, Christopher Z W Lee, Zhigang Li, Jian He, Yandong Gong, Zongcheng Li, Jie Zhou, Yang Zeng, Xianlong Li, Yanli Ni, Zhijie Bai, Chen Liu, Na Li, Honghao Ma, Dong Wang, Yu Lan*, Florent Ginhoux*, Rui Zhang*, Bing Liu*. Transcriptomic landscape of circulating mononuclear phagocytes in Langerhans cell histiocytosis at the single-cell level.Blood.2021.138(14).1237-1248.SCI |
20. Hongyun Lian, Ang Wei, Lejian He, Ying Yang, Honghao Ma, Liping Zhang, Yitong Guan, Qing Zhang, Dong Wang, Zhigang Li*, Rui Zhang*, Tianyou Wang*. Clinical Analysis of Pediatric Systemic Juvenile Xanthogranulomas: A Retrospective Single-Center Study. .Frontiers in pediatrics..2021.9.672547.SCI |
21. Sitong Chen, Ang Wei, Honghao Ma, Liping Zhang, Hongyun Lian, Yunze Zhao, Qing Zhang, Fenfen Cheng, Dong Wang, Tianyou Wang, Zhigang Li, Rui Zhang*.Clinical Features and Prognostic Factors of Children with Chronic Active Epstein-Barr Virus Infection: A Retrospective Analysis of a Single Center. .The Journal of pediatrics.2021.238.268-274.SCI |
22. Honghao Ma#, Liping Zhang#, Ang Wei, Jun Yang, Dong Wang, Qing Zhang, Yunze Zhao, Sitong Chen, Hongyun Lian, Li Zhang, Chunju Zhou, Maoquan Qin, Zhigang Li*, Tianyou Wang*, Rui Zhang*.Outcome of L-DEP regimen for treatment of pediatric chronic active Epstein-Barr virus infection..Orphanet journal of rare diseases.2021.16(1).269.SCI |
23. Ang Wei#, Honghao Ma#, Liping Zhang, Zhigang Li, Yitong Guan, Qing Zhang, Dong Wang, Hongyun Lian, Rui Zhang*, Tianyou Wang.*.Clinical analysis of chronic active EBV infection with coronary artery dilatation and a matched case-control study.Orphanet journal of rare diseases.2021.16(1).50.SCI |
24. Qing Zhang#, Yun-Ze Zhao#, Hong-Hao Ma, Dong Wang, Nan Zhang, Zhi-Gang Li, Rui Zhang* .Successful rescue of a lethal Griscelli syndrome type 2 presenting with neurological involvement and hemophagocytic lymphohistiocytosis: a case report. .BMC pediatrics.2021. 21 (1) .253.SCI |
25. Xia Lu#, Ang Wei#, Xu Yang, Jun Liu, Siqi Li, Ying Kan, Wei Wang, Tianyou Wang, Rui Zhang*, Jigang Yang*. The Role of Pre-therapeutic 18F-FDG PET/CT in Pediatric Hemophagocytic Lymphohistiocytosis With Epstein-Barr Virus Infection..Frontiers in medicine..2021.8.836438.SCI |
26. Honghao Ma#, Rui Zhan#g, Liping Zhang#, Ang Wei, Xiaoxi Zhao, Ying Yang, Wei Liu, Zhigang Li*, Maoquan Qin*, Tianyou Wang*. Treatment of pediatric primary hemophagocytic lymphohistiocytosis with the HLH-94/2004 regimens and hematopoietic stem cell transplantation in China..Annals of hematology.2020.99 (10).2255-2263..SCI |
27. 10. Yun-Ze Zhao, Zhi-Gang Li, Li Zhang, Hong-Yun Lian, Hong-Hao Ma, Dong Wang, Xiao-Xi Zhao, Qing Zhang, Tian-You Wang, Rui Zhang. .L‐DEP regimen salvage therapy for paediatric patients with refractory Epstein‐Barr virus‐associated haemophagocytic lymphohistiocytosis..British Journal of Haematology.2020.191(3).453-459.SCI |
28. 12. Ang Wei#, Honghao Ma#, Zhigang Li, Liping Zhang, Qing Zhang, Dong Wang, Hongyun Lian, Rui Zhang*, Tianyou Wang*.Short-term effectiveness of ruxolitinib in the treatment of recurrent or refractory hemophagocytic lymphohistiocytosis in children.International Journal of Hematology.2020.112(4).568-576.SCI |
29. Wei A, Ma H, Li Z, Zhang L, Zhang R*, Wang T*.Type-IV Glycogen Storage Disease Associated with Hemophagocytic lymphositiocytosis: a case report..Journal of Pediatric Hematology and Oncology.2020.42(5).368-369.SCI |
30. 魏昂、马宏浩、张利平、吴润晖、张蕊*,王天有*.以噬血细胞综合症为首发表现的肝炎相关再生障碍性贫血5例临床分析.中华儿科杂志.2020.58(3).213-217.核心期刊 |
31. 张晴 崔蕾, 马宏浩, 王冬, 赵云泽, 王天有, 李志刚*, 张蕊*.血浆及全血EB病毒DNA对EB病毒相关噬血细胞性淋巴组织细胞增生症患儿预后的影响.中华实用儿科临床杂志.2020.35.1139-43.核心期刊 |
32. Guang Hua Zhu#, Li Ping Zhang#, Zhi Gang Li, Ang Wei, Ying Yang, Yu Tian, Hong Hao Ma, Dong Wang, Xiao Xi Zhao, Yun Ze Zhao, Na Li, Wei Liu, Tian You Wang*, Rui Zhang*. Associations between PRF1 Ala91Val polymorphism and risk of hemophagocytic lymphohistiocytosis: a meta-analysis based on 1366 subjects.World J Pediatr.2020.16(6).598-606.SCI |
33. Wei A, Ma H, Li Z, Zhang L, Zhang R*, Wang T*.Type-IV Glycogen Storage Disease Associated with Hemophagocytic lymphositiocytosis: a case report.Journal of Pediatric Hematology and Oncology.2020.42(5).368-369.SCI |
34. Chellapandian D, Hines MR, Zhang R, Jeng M, van den Bos C, Santa-María López V, Lehmberg K, Sieni E, Wang Y, Nakano T, Williams JA, Fustino NJ, Astigarraga I, Dunkel IJ, Abla O, van Halteren AGS, Pei D, Cheng C, Weitzman S, Sung L, Nichols KE.A multicenter study of patients with multisystem Langerhans cell histiocytosis who develop secondary hemophagocytic lymphohistiocytosis.Cancer.2019.125(6).963-971.SCI |
35. Zhang L, Li Z, Liu W, Ma H, Wang T*, Zhang R*.Genetic characterization of pediatric primary hemophagocytic lymphohistiocytosis in China: a single-center study.Ann Hematol.2019.98(10).2303-231.SCI |
36. Zhao XX, Lian HY, Zhang L, Ma HH, Wang D, Zhao YZ, Liu ZW, Wang TY, Zhang R*, Li ZG*.Significance of serum ferritin level in hemophagocytic lymphohistiocytosi.Int J Lab Hematol.2019.41(4).503-508.SCI |
37. 廉红云,张莉,李志刚,马宏浩,王冬,赵云泽,赵晓曦,王天有,张蕊*.儿童颅面骨受累的朗格罕细胞组织细胞增生症临床分析.中华实用儿科临床杂志.2019.34(15).1151-1155.核心期刊 |
38. Wei A, Ma H, Li Z, Zhang L, Zhang R*, Wang T*.Successful treatment of a child with idiopathic multicentric Castleman disease associated with hemophagocytic lymphohistiocytosis using tocilizumab.Pediatr Blood Cancer.2019.66(7).e27759.SCI |
39. Yun‐Ze Zhao, Hua Cheng, Chang‐Hong Ding, Hong‐Hao Ma, Tong‐Li Han, Jiu‐Wei Li, Dong Wang, Zhi‐Gang Li, Tian‐You Wang, Rui Zhang*.Neurological Abnormality Could be the First and Only Symptom of Familial Hemophagocytic Lymphohistiocytosis, Report of Two Families..Chinese Medical Journal.2018.131(24).3004-3006.SCI |
40. Dong Wang, Lei Cui, Zhi-Gang Li, Li Zhang, Hong-Yun Lian, Hong-Hao Ma, Yun-Ze Zhao, Xiao-Xi Zhao, Tian-You Wang, Rui Zhang*.Clinical Research of Pulmonary Langerhans Cell Histiocytosis in Children. .Chinese Medical Journal.2018.131(15).1794-1798.SCI |
41. Yun-Ze Zhao, Lei Cui, Zhi-Gang Li, Li Zhang, Hong-Yun Lian, Hong-Hao Ma, Dong Wang, Xiao-Xi Zhao, Tian-You Wang, Rui Zhang*.Central Nervous System Involvement in 179 Chinese Children with Hemophagocytic Lymphohistiocytosis.Chinese Medical Journal.2018.131(15).1786-1792.SCI |
42. 马宏浩, 王天有, 张莉, 廉红云, 王冬, 赵云泽, 赵晓曦, 张蕊*.儿童EB病毒相关噬血细胞性淋巴组织细胞增生症的预后相关危险因素分析.北京医学.2018.40(7).622-628.核心期刊 |
43. 马宏浩, 王天有, 张莉, 廉红云, 王冬, 赵云泽, 赵晓曦, 张蕊*.儿童甲状腺受累的朗格罕细胞组织细胞增生症 8例临床分析.中华实用儿科临床杂志.2017.32(20).1552-1555.核心期刊 |
44. 张莉,廉红云,马宏浩,高超,王冬,王天有,张蕊*.BRAF基因V600E突变在儿童朗格罕细胞组织细胞增生症中的临床意义.中国小儿血液与肿瘤杂志.2017.22(4).190-193.核心期刊 |
45. 张莉,廉红云,马宏浩,高超,王冬,王天有,张蕊*.儿童朗格罕细胞组织细胞增生症217例临床分析.中华实用儿科临床杂志.2017.32(15).1141-1144.核心期刊 |
46. 赵云泽,王天有,张莉,廉红云,马宏浩,王冬,赵晓曦,张蕊*.中枢神经系统受累对噬血细胞性淋巴组织细胞增生症(HLH)患儿预后的影响.中华实用儿科临床杂志.2016.31(22).1737-1740.核心期刊 |
47. Rui Zhang, Ling Jin, Hua Cheng, Jing Yang, Yan-Long Duan, Shuang Huang, Yong-Hong Zhang*.Reversible Posterior Leukoencephalopathy Syndrome Sometimes Could be Irreversible: A Case Following Tumor Lysis Syndrome in Childhood Burkitt’s Lymphoma.Chinese Medical Journal.2016.31(22).480-483.SCI |
48. 张莉, 廉红云, 马宏浩, 王冬, 高超, 王天有, 张蕊*.单器官受累郎格罕细胞组织细胞增生症112例.中华实用儿科临床杂志.2016.31(15).1172-1174.核心期刊 |
49. 马宏浩,王天有,张莉,廉红云,王冬,赵云泽,赵晓曦,张蕊*.儿童难治性EB病毒相关噬血细胞性淋巴组织细胞增生症-治疗中病情暴发发3例并文献综述.中华实用儿科临床杂志.2016.31(22).1745-1748.核心期刊 |